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Paraparesis
Paraparesis waa nooc khafiif ah oo ah curyaannimo darafka hoose kaas oo ah hidde ama uu sababay fayras. Xanuunka iyo murgacashada waxaa lagu yarayn karaa daawo, iyo daaweynta jirka iyo jimicsigu waxay ilaalin karaan dhaqdhaqaaqa iyo xoogga muruqa.
Paraparesis, waa maxay?
Qeexitaanka paraparesis
Paraparesis waa erey caafimaad oo loo isticmaalo sifeynta daciifnimada horusocodka oo ay weheliso muruqyada muruqyada (daciifnimada laf -dhabarka) ee darajooyinka hoose. Waa nooc ka khafiifsan paraplegia (curyaannimo addimada hoose).
Paraparesis Spastic waa koox cudurro ah oo ay sababaan cillado ku dhaca laf -dhabarka.
Noocyada paraparesis
Paraparesis Spastic wuxuu noqon karaa mid la iska dhaxlo ama uu sababo fayras.
Paraparesis hidde ah oo dhaxal ah
Waxay u qaybsan yihiin kuwo aan cakiranayn (ama daahir ah) oo murugsan (ama kakan) marka ay calaamadaha caadiga ah ee laf -dhabarta hoose ay la socdaan calaamado kale sida:
- Cerebellar atrophy: hoos u dhaca mugga ama cabbirka cerebellum
- Callosum corpus dhuuban (isgoyska u dhexeeya labada dhinac ee maskaxda)
- Ataxia: khalkhalka isuduwidda dhaqdhaqaaqa sababtuna tahay dhaawaca cerebellum
Hidda ahaan, paraparesis spastic waxaa loo kala saari karaa iyadoo loo eegayo qaabka gudbintooda:
- Xukun: waxaa ku filan in cillad -xumadu ay saameyso hal nuqul oo hidde -sidaha ah si cudurku u kobco.
- Recessive: cilladdu waa inay saamaysaa labada nuqul ee hidda -wadaha, mid kasta oo laga dhaxlay mid ka mid ah waalidka, si cudurku u kobco.
- X-ku xiran: Ragga, oo leh kaliya hal koromosoom X, ayaa cudurka qaada haddii ay ku qaadaan cillad aan caadi ahayn hal koobi oo ah hiddasidaha.
Paraparesis Tropical spastic
Sidoo kale loo yaqaanno HTLV-1 myelopathy la xiriira, waa cillad si tartiib tartiib ah u kordheysa oo ku dhacda xudunta laf-dhabarta oo ay keento nooca fayruska lymphotrophic T nooca 1 (HTLV-1).
Sababaha paraparesis spastic
Paraparesis spastic pararedis waxay noqon kartaa natiijada noocyo badan oo cillado hidde ah ama iskood u kobci kara. Waqtigan xaadirka ah, 41 nooc oo ah paraparesis spastic paraparesis oo la iska dhaxlo ayaa la yaqaan, laakiin kaliya 17 kaas oo loo aqoonsaday hidda -wadaha mas'uulka ka ah.
Paraparesis spastic paraparesis waxaa sababa fayraska HTLV-1.
cudurka
Paraparesis spastic paraparesis ayaa la tuhunsan yahay sababtoo ah jiritaanka taariikhda qoyska iyo calaamad kasta oo paraparesis ah.
Baadhitaanku wuxuu marka hore ku salaysan yahay ka reebitaanka sababaha kale ee suurtogalka ah:
- Adrenoleukodystrophy, oo ah cudur ku dhaca X-neurodegenerative
- Cagaarshow Multiple
- Cudur ku lug leh neuronka sare ee maskaxda (sclerosis lateral sclerosis ama amyotrophic lateral sclerosis)
- HIV ama HTLV-1 caabuq
- Yaraanta fitamiin B12, fitamiin E ama naxaas
- Spinocerebellar ataxia, waa cudur neuromuscular oo saameeya cerebellum
- Xanuunka laf -dhabarka ee laf -dhabarka
- Buro dhuuxa lafta
- Cervicoarthritis myelopathy, cidhiidhi ah kanaalka laf -dhabarta oo ciriiriya xadhigga afka ilmo -galeenka
Ciladeynta paresis spastic ee la iska dhaxlo ayaa mararka qaarkood lagu sameeyaa baaritaanka hidde -sidaha.
Dadka ay khusayso
Paraparesis -ka dhaxalku wuxuu u saameeyaa labada jinsi si aan kala sooc lahayn wuxuuna ku dhici karaa da 'kasta. Waxay ku dhacdaa 3 ilaa 10 qof 100 kiiba.
Waxyaabaha khatarta
Khatarta ah in uu yeesho paraparesis dhaxal ah ayaa ka weyn haddii ay jirto taariikh qoys. Marka laga hadlayo paraparesis kulaylaha kulaylaha ah, halista qaadista cudurku waxay la xiriirtaa halista ah inuu ku dhaco fayraska HTLV-1, kaas oo lagu kala qaado taabashada galmada, isticmaalka daroogada sharci darrada ah ama xididdada dhiigga. Waxa kale oo laga gudbin karaa hooyada ilaa ilmaha iyada oo loo marayo naas -nuujinta.
Astaamaha paraparesis
Spasticity of addimada hoose
Spasticity waxaa lagu qeexaa kororka is -beddelka tonic -ka, taas oo ah in la yiraahdo muruq -celinta muruqa fekerka oo la buunbuuniyey. Waxay keentaa murqo aad u sarreeya oo sababi kara xanuun iyo murgacasho, waxayna sababi kartaa awood -darro shaqaysa addimada.
Hoos -u -dhaca mootada
Dadka qaba paraparesis badiyaa way ku adag tahay socodka. Way safri karaan sababtoo ah waxay u muuqdaan inay ku socdaan lugahooda, cagahooduna u jeedaan gudaha. Kabaha inta badan waxay ku waxyeeloobaan suulka weyn. Dadku badiyaa waxay ku dhibtoonayaan inay jaranjarooyinka ama dhaadhacyada ka soo degaan, inay kursi ama baabuur galaan, labistaan, iyo qurxiyaan.
Asthenia
Asthenia waa daal aan caadi ahayn marka ay sii socoto xitaa nasashada kadib. Waxay keentaa dareen ah inaanad awoodin inaad fuliso hawl maalmeedka.
Xanuunada hordhaca ah
Luminta dareenka booska cagaha iyo suulasha
Calaamadaha kale
Foomamka aan cakiranayn, waxaan kaloo arki karnaa:
- Dhibaatooyin khafiif ah oo dareen -gariir leh
- Astaamaha kaadida (ceshad la'aanta)
- Cagaha bannaan
Qaabab adag,
- Ataxia, khalkhalka isuduwidda dhaqdhaqaaqa asalka neerfaha
- Amyotrophie
- Hoos -u -dhaca indhaha
- Midabka indhaha ee indhaha
- Hoos u dhaca maskaxda
- Calaamadaha Extrapyramidal
- Asaasaqa
- Dhago la'aanta
- Peripheral neuropathy
- Epilepsy
Daaweynta Paraparesis
Daaweyntu waa calaamado, oo ay ku jiraan daawaynta si loo yareeyo buufiska.
- Daawaynta dawooyinka nidaamsan: baclofen, dantrolene, clonazepam, diazepam, tizanidine, benzodiazepines
- Daaweynta maxalliga ah: xannibaad suuxin, sun botulinum (intromuscular -ka la beegsanayo), aalkolo, qalliin (neurotomy xulasho)
Daaweynta jirka iyo jimicsiga ayaa kaa caawin kara joogteynta dhaqdhaqaaqa iyo xoogga muruqa, hagaajinta dhaqdhaqaaqa kala duwan iyo dulqaadka, yareynta daalka, iyo ka hortagga murqaha.
Bukaanjiifka qaar ayaa ka faa'iideysta adeegsiga kabaha, bakoorad ama usha.
Wixii paraparesias spastic paraparesias, dhowr daaweyn ayaa waxtar u leh la -dagaallanka fayraska:
- Interferon alfa
- Immunoglobulin (xidid -gale)
- Corticosteroids (sida methylprednisolone afka)
Ka hortag paraparesis
Si looga fogaado in uu ku dhaco paraparesis kulaylaha kulaylaha, waa in la yareeyaa taabashada fayraska HTLV-1. Waxaa lagu kala qaadaa:
- Xiriirka galmada
- Isticmaalka daroogada xaaraanta ah ee xididka
- Soo -gaadhista dhiigga
Waxay hooyadu u gudbin kartaa naas -nuujinta. Waxay aad ugu badan tahay dhillooyinka, duritaanka dadka isticmaala daroogada, dadka ku jira dhiig -baxa iyo dadka ku nool gobollada qaarkood oo ay ku jiraan meel u dhow dhulbaraha, koonfurta Japan iyo Koonfurta Ameerika.
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